Melkersson-Rosenthal Syndrome in Pediatric Age Group

Gürkan Kayabaşoğlu, Mahmut Sinan Yılmaz, Ali Fuat Varlı, Mehmet Güven
1.178 321

Abstract


Melkersson-Rosenthal Syndrome (MRS) is a disease characterized by peripheral facial paralysis, facial edema and fissured tongue. Appearance of this triad is rare, generally monosymptomatic or oligosymptomatic involvement is observed and difficulties or delays in diagnosis can occur due to scarcity of the disease. One or two of the findings and presence of cheilitis granulomatosa in biopsy are sufficient for the diagnosis. Melkersson Rosenthal Syndrome should be considered in differential diagnosis of recurrent facial paralysis. Although findings of the syndrome can regress spontaneously or with medical treatment, it can take a progressive course in some patients, requiring surgical treatment (facial nerve decompression). In this article a pediatric case with diagnosis of Melkersson Rosenthal Syndrome is presented.

Keywords


Melkersson-Rosenthal syndrome, orofacial edema, recurrent facial paralysis.

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References


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